Isolated left atrial amyloidosis: Acute premitral stenosis secondary to spontaneous intramural left atrial hemorrhagic dissection
Edibam, C., Playford, D., Texler, M., & Edwards, M. (2006). Isolated left atrial amyloidosis: Acute premitral stenosis secondary to spontaneous intramural left atrial hemorrhagic dissection. Journal of the American Society of Echocardiography, 19(7), 938. doi:10.1016/j.echo.2006.01.028
This case presentation describes the very rare condition of isolated atrial amyloidosis and it’s associated complications. A 53-year-old male presented to hospital in severe pulmonary edema secondary to spontaneous intramural left atrial hemorrhage and subsequent wall dissection causing acute “pre-mitral valve” obstruction. The patient was subsequently found to have AL subtype amyloid, which has never before been reported in isolated atrial amyloidosis. The prognosis is poor in AL type amyloidosis with cardiac involvement.